KMID : 0356920070520030363
|
|
Korean Journal of Anesthesiology 2007 Volume.52 No. 3 p.363 ~ p.366
|
|
Anesthesia for a Patient with Osler-Weber-Rendu Syndrome -A case report-
|
|
Lee Su-Nam
Kim Jin-Kang Sohn Dong-Il Lee Ji-Heui Lee Yong-Seok Lee So-Young
|
|
Abstract
|
|
|
Hereditary haemorrhagic telangiectasia (HHT), or Osler-Weber-Rendu syndrome is an autosomal dominant disorder characterized by recurrent epistaxis, mucocutaneous telangiectasias, and visceral involvement including arteriovenous malformations that may develop in any organ, especially in the lung, brain, liver and GI tract. Early screening and regular follow up of patients with HHT are important to minimize the risk of development of serious sequelae. We report a case of 46-year-old female patient who had "suspected HHT" and review the literature on this rare disease.
|
|
KEYWORD
|
|
arteriovenous malformation, hereditary haemorrhagic telangiectasia, Osler-Weber-Rendu syndrome
|
|
FullTexts / Linksout information
|
|
|
|
Listed journal information
|
|
|